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Lesley C. Adès

Sydney Children’s Hospitals Network · AU
Area of research
Genetics · Pulmonary and Respiratory Medicine
Research interest
Research interests include Connective tissue disorders research, Aortic Disease and Treatment Approaches, Genomic variations and chromosomal abnormalities, and Genomics and Rare Diseases.
h-index
46
citations
8,748
works
130
NIH funding
primary concept
Medicine
email

Recent publications

Genomic autopsy to identify underlying causes of pregnancy loss and perinatal death
Nature Medicine 2023cited by 62position: middledoi
PSMC3 proteasome subunit variants are associated with neurodevelopmental delay and type I interferon production
Science Translational Medicine 2023cited by 35position: middledoi
Connective tissue presentation in two families expands the phenotypic spectrum of <i>PYROXD1</i> disorders
Human Molecular Genetics 2023cited by 6position: middledoi
Whole exome and genome sequencing in mendelian disorders: a diagnostic and health economic analysis
European Journal of Human Genetics 2022cited by 115position: middledoi
Standardized practices for RNA diagnostics using clinically accessible specimens reclassifies 75% of putative splicing variants
Genetics in Medicine 2021cited by 103position: middledoi
Feasibility of Ultra-Rapid Exome Sequencing in Critically Ill Infants and Children With Suspected Monogenic Conditions in the Australian Public Health Care System
JAMA 2020cited by 233position: middledoi
Missense variants in <i>TAF1</i> and developmental phenotypes: Challenges of determining pathogenicity
Human Mutation 2019cited by 28position: middledoi
Clinical Validity of Genes for Heritable Thoracic Aortic Aneurysm and Dissection
Journal of the American College of Cardiology 2018cited by 298position: middledoi
Clinical history and management recommendations of the smooth muscle dysfunction syndrome due to ACTA2 arginine 179 alterations
Genetics in Medicine 2018cited by 82position: middledoi
Spondyloenchondrodysplasia Due to Mutations in ACP5: A Comprehensive Survey
Journal of Clinical Immunology 2016cited by 104position: middledoi
Mutations in MAP3K7 that Alter the Activity of the TAK1 Signaling Complex Cause Frontometaphyseal Dysplasia
The American Journal of Human Genetics 2016cited by 72position: middledoi
HUWE1 mutations in Juberg-Marsidi and Brooks syndromes: the results of an X-chromosome exome sequencing study
BMJ Open 2016cited by 52position: middledoi
<i>RASA1</i>Mutations and Associated Phenotypes in 68 Families with Capillary Malformation-Arteriovenous Malformation
Human Mutation 2013cited by 290position: middledoi
Extreme Growth Failure is a Common Presentation of Ligase IV Deficiency
Human Mutation 2013cited by 86position: middledoi
In-Frame Mutations in Exon 1 of SKI Cause Dominant Shprintzen-Goldberg Syndrome
The American Journal of Human Genetics 2012cited by 110position: middledoi
Evaluation of Clinical Manifestations in Patients with Severe Lymphedema with and without CCBE1 Mutations
Molecular Syndromology 2012cited by 50position: middledoi

Grants

No grants ingested yet.

Frequent collaborators

J. Schmidtke · Medizinische Hochschule Hannover1 papers (2012–2012) · 1 papers (2016–2016)Sara K. Pittman · UCLA Medical Center1 papers (2023–2023)Lut Van Laer · University of Antwerp1 papers (2018–2018) · 1 papers (2018–2018)Hülya Kayserili · University of Exeter1 papers (2012–2012)P. Dane Witmer · Johns Hopkins University1 papers (2018–2018)Catherine Francis · Guy's and St Thomas' NHS Foundation Trust1 papers (2018–2018)Rajarshi Ghosh · National Institutes of Health1 papers (2018–2018)Carlo Bellini · University of North Texas1 papers (2012–2012)Gregory Dziaduch · The University of Sydney1 papers (2023–2023)Michael J. Friez · Medical University of South Carolina1 papers (2016–2016) · 1 papers (2016–2016)Conrad C. Weihl · Washington University in St. Louis1 papers (2023–2023)Harry C. Dietz · Johns Hopkins University1 papers (2018–2018) · 1 papers (2016–2016)Bart Loeys · Erasmus MC1 papers (2018–2018)Leema Robert · St Thomas' Hospital1 papers (2018–2018)Michael Field · UNSW Sydney1 papers (2016–2016)Patrick Tarpey · Cambridge University Hospitals NHS Foundation Trust1 papers (2016–2016)