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Johnathan Cooper‐Knock

Utrecht University · NL
Area of research
Neurology · Genetics
Research interest
Research interests include Amyotrophic Lateral Sclerosis Research, Neurogenetic and Muscular Disorders Research, Neurological diseases and metabolism, and Parkinson's Disease Mechanisms and Treatments.
h-index
40
citations
7,552
works
175
NIH funding
primary concept
email

Recent publications

Oligogenic structure of amyotrophic lateral sclerosis has genetic testing, counselling and therapeutic implications
Journal of Neurology Neurosurgery & Psychiatry 2025cited by 12position: middledoi
Single-cell polygenic risk scores dissect cellular and molecular heterogeneity of complex human diseases
Nature Biotechnology 2025cited by 9position: middledoi
An observational study of pleiotropy and penetrance of amyotrophic lateral sclerosis associated with CAG-repeat expansion of ATXN2
European Journal of Human Genetics 2025cited by 6position: middledoi
Extreme exercise in males is linked to mTOR signalling and onset of amyotrophic lateral sclerosis
Brain 2025cited by 3position: middledoi
Optimised machine learning for time-to-event prediction in healthcare applied to timing of gastrostomy in ALS: a multi-centre, retrospective model development and validation study
EBioMedicine 2025cited by 0position: lastdoi
Considerations in the search for epistasis
Genome biology 2024cited by 16position: middledoi
Guidance for clinical management of pathogenic variant carriers at elevated genetic risk for ALS/FTD
Journal of Neurology Neurosurgery & Psychiatry 2024cited by 15position: middledoi
Rare and common genetic determinants of mitochondrial function determine severity but not risk of amyotrophic lateral sclerosis
Heliyon 2024cited by 11position: lastdoi
Mutations in the tail and rod domains of the neurofilament heavy‐chain gene increase the risk of <scp>ALS</scp>
Annals of Clinical and Translational Neurology 2024cited by 5position: middledoi
Mechanism-Free Repurposing of Drugs For&amp;nbsp;C9orf72-related ALS/FTD Using Large-Scale Genomic Data
SSRN Electronic Journal 2024cited by 0position: middledoi
Mechanism-Free Repurposing of Drugs For&amp;nbsp;C9orf72-Related ALS/FTD Using Large-Scale Genomic Data
SSRN Electronic Journal 2024cited by 0position: middledoi
Clinical testing panels for ALS: global distribution, consistency, and challenges
Amyotrophic Lateral Sclerosis and Frontotemporal Degeneration 2023cited by 17position: middledoi
Large-scale analyses of CAV1 and CAV2 suggest their expression is higher in post-mortem ALS brain tissue and affects survival
Frontiers in Cellular Neuroscience 2023cited by 5position: middledoi
Genome-wide identification of the genetic basis of amyotrophic lateral sclerosis
Neuron 2022cited by 121position: middledoi
Genome-wide study of DNA methylation shows alterations in metabolic, inflammatory, and cholesterol pathways in ALS
Science Translational Medicine 2022cited by 91position: middledoi
Structural variation analysis of 6,500 whole genome sequences in amyotrophic lateral sclerosis
npj Genomic Medicine 2022cited by 43position: middledoi
Whole-genome sequencing reveals that variants in the Interleukin 18 Receptor Accessory Protein 3′UTR protect against ALS
Nature Neuroscience 2022cited by 40position: middledoi
Multiomic analysis reveals cell-type-specific molecular determinants of COVID-19 severity
Cell Systems 2022cited by 37position: middledoi
Telomere length analysis in amyotrophic lateral sclerosis using large-scale whole genome sequence data
Frontiers in Cellular Neuroscience 2022cited by 9position: middledoi
Author Correction: Common and rare variant association analyses in amyotrophic lateral sclerosis identify 15 risk loci with distinct genetic architectures and neuron-specific biology
Nature Genetics 2022cited by 4position: middledoi
Mitochondrial function determines severity but not risk of amyotrophic lateral sclerosis
bioRxiv (Cold Spring Harbor Laboratory) 2022cited by 1position: lastdoi
Large-scale Analyses of CAV1 and CAV2 Suggest Their Expression is Higher in Post-mortem ALS Brain Tissue and Affects Survival
medRxiv 2022cited by 0position: middledoi
Common and rare variant association analyses in amyotrophic lateral sclerosis identify 15 risk loci with distinct genetic architectures and neuron-specific biology
Nature Genetics 2021cited by 538position: middledoi
Physical exercise is a risk factor for amyotrophic lateral sclerosis: Convergent evidence from Mendelian randomisation, transcriptomics and risk genotypes
EBioMedicine 2021cited by 108position: middledoi
Enrichment of SARM1 alleles encoding variants with constitutively hyperactive NADase in patients with ALS and other motor nerve disorders
eLife 2021cited by 82position: middledoi
Advances in the genetic classification of amyotrophic lateral sclerosis
Current Opinion in Neurology 2021cited by 24position: firstdoi
Spatiotemporal Proteomic Analysis of Stress Granule Disassembly Using APEX Reveals Regulation by SUMOylation and Links to ALS Pathogenesis
Molecular Cell 2020cited by 258position: middledoi
Rare Variant Burden Analysis within Enhancers Identifies CAV1 as an ALS Risk Gene
Cell Reports 2020cited by 42position: firstdoi
Mutations in the Glycosyltransferase Domain of GLT8D1 Are Associated with Familial Amyotrophic Lateral Sclerosis
Cell Reports 2019cited by 79position: firstdoi
Targeted Genetic Screen in Amyotrophic Lateral Sclerosis Reveals Novel Genetic Variants with Synergistic Effect on Clinical Phenotype
Frontiers in Molecular Neuroscience 2017cited by 32position: firstdoi

Grants

No grants ingested yet.

Frequent collaborators

Pamela J. Shaw · Sheffield Health and Social Care NHS Foundation Trust6 papers (2012–2025)Sai Zhang · Shandong Normal University6 papers (2021–2025)Calum Harvey · University of Sheffield5 papers (2021–2024)Thomas Julian · University of Manchester5 papers (2021–2025)M Snyder · Cardiovascular Institute of the South5 papers (2021–2025)Tobias Moll · University of Sheffield4 papers (2021–2024)Alfredo Iacoangeli · King's College London4 papers (2021–2024)Marcel Weinreich · German Cancer Research Center3 papers (2022–2025)Jan H. Veldink · University Medical Center Utrecht3 papers (2021–2024)Kevin P. Kenna · Utrecht University3 papers (2021–2024)Christopher McDermott · Lancashire Teaching Hospitals NHS Foundation Trust2 papers (2012–2017)Dan E. Arking · IRCCS Materno Infantile Burlo Garofolo2 papers (2022–2024)Ramona A.J. Zwamborn · Utrecht University2 papers (2022–2024)Philip S. Tsao · Stanford University2 papers (2022–2025)John P. Quinn · UK Dementia Research Institute2 papers (2022–2024)Kristel van Eijk · Utrecht University2 papers (2022–2024) · 2 papers (2022–2024)Janine Kirby · Instituto de Investigaciones Biomédicas Sols-Morreale2 papers (2012–2017)Stephen A. Goutman · Michigan United2 papers (2021–2024)Paul J. Hop · Utrecht University2 papers (2022–2024)