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Bryce A. Mendelsohn

Kaiser Permanente Oakland Medical Center · US
Area of research
Genetics · Molecular Biology
Research interest
Research interests include Genomics and Rare Diseases, Mitochondrial Function and Pathology, Genomic variations and chromosomal abnormalities, and RNA Research and Splicing.
h-index
26
citations
2,069
works
70
NIH funding
primary concept
email

Recent publications

The Spectrum of Neurologic Phenotypes Associated With <scp><i>NUS1</i></scp> Pathogenic Variants: A Comprehensive Case Series
Annals of Neurology 2025cited by 6position: middledoi
Adaptor protein 2 sigma subunit ( <i>AP2S1</i> ) variants associated with neurodevelopmental disorders
medRxiv 2024cited by 1position: middledoi
Diagnostic yield of pediatric and prenatal exome sequencing in a diverse population
npj Genomic Medicine 2023cited by 42position: middledoi
A multinational study of acute and long‐term outcomes of Type 1 galactosemia patients who carry the <scp>S135L</scp> (c.<scp>404C</scp> &gt; T) variant of <scp><i>GALT</i></scp>
Journal of Inherited Metabolic Disease 2022cited by 11position: middledoi
DLG4-related synaptopathy: a new rare brain disorder
Genetics in Medicine 2021cited by 52position: middledoi
Application of full-genome analysis to diagnose rare monogenic disorders
npj Genomic Medicine 2021cited by 52position: middledoi
SLC35A2‐CDG: Functional characterization, expanded molecular, clinical, and biochemical phenotypes of 30 unreported Individuals
Human Mutation 2019cited by 66position: middledoi
Allogeneic HSCT for adult-onset leukoencephalopathy with spheroids and pigmented glia
Brain 2019cited by 61position: middledoi
Deleterious de novo variants of X‐linked <i>ZC4H2</i> in females cause a variable phenotype with neurogenic arthrogryposis multiplex congenita
Human Mutation 2019cited by 46position: middledoi
A high-throughput screen of real-time ATP levels in individual cells reveals mechanisms of energy failure
PLoS Biology 2018cited by 60position: firstdoi
Clinical Report: Warsaw Breakage Syndrome with small radii and fibulae
American Journal of Medical Genetics Part A 2017cited by 57position: middledoi
De novo, deleterious sequence variants that alter the transcriptional activity of the homeoprotein PBX1 are associated with intellectual disability and pleiotropic developmental defects
Human Molecular Genetics 2017cited by 57position: middledoi
The Role of Mitochondrially Derived ATP in Synaptic Vesicle Recycling
Journal of Biological Chemistry 2015cited by 332position: middledoi
Exome sequencing in 32 patients with anophthalmia/microphthalmia and developmental eye defects
Clinical Genetics 2014cited by 70position: middledoi

Grants

No grants ingested yet.

Frequent collaborators

Ken Nakamura · Gladstone Institutes2 papers (2015–2018)Anne Slavotinek · Cincinnati Children's Hospital Medical Center2 papers (2017–2021)Christopher P. Hess · University of California, San Francisco1 papers (2019–2019)Martin Kampmann · University Memory and Aging Center1 papers (2018–2018)Daniah Beleford · University of California, San Francisco1 papers (2021–2021)Katharine Yu · Nkarta Therapeutics (United States)1 papers (2018–2018)Monica Penon‐Portmann · Seattle Children's Hospital1 papers (2021–2021)Gabriel N. Mannis · Stanford University1 papers (2019–2019)Zhongxia Qi · University of California, San Francisco1 papers (2021–2021)Divya Pathak · Guru Gobind Singh Indraprastha University1 papers (2015–2015)Hwajin Kim · Columbia University1 papers (2015–2015)Stephen K. Chow · University of California, San Francisco1 papers (2021–2021)William C. Hyun · University of California, San Francisco1 papers (2018–2018)Hazel Perry · University of California, San Francisco1 papers (2021–2021)Wei Lin · Gladstone Institutes1 papers (2015–2015)Daniela Pucciarelli · University of California, San Francisco1 papers (2018–2018)K. Wong · University of California, San Francisco1 papers (2021–2021)Jingwei Yu · Guangzhou University of Chinese Medicine1 papers (2021–2021)Michelle Verghese · University of Chicago1 papers (2021–2021)Maxine Nelson · MetroHealth1 papers (2018–2018)