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Johann Böhm

St Thomas' Hospital ·
Area of research
Cardiology and Cardiovascular Medicine · Molecular Biology
Research interest
Research interests include Biology, Genetics, Myopathy, Mutation, ORAI1, and Frameshift mutation.
h-index
citations
507
works
8
NIH funding
primary concept
email

Recent publications

ORAI1 inhibition as an efficient preclinical therapy for tubular aggregate myopathy and Stormorken syndrome
JCI Insight 2024cited by 6position: lastdoi
Heterozygous frameshift variants in HNRNPA2B1 cause early-onset oculopharyngeal muscular dystrophy
Nature Communications 2022cited by 43position: middledoi
Pathogenic Variants in the Myosin Chaperone UNC-45B Cause Progressive Myopathy with Eccentric Cores
The American Journal of Human Genetics 2020cited by 46position: middledoi
A Novel TTC19 Mutation in a Patient With Neurological, Psychological, and Gastrointestinal Impairment
Frontiers in Neurology 2019cited by 20position: middledoi
STIM1 over-activation generates a multi-systemic phenotype affecting the skeletal muscle, spleen, eye, skin, bones and immune system in mice
Human Molecular Genetics 2018cited by 50position: lastdoi
Dihydropyridine receptor (DHPR, CACNA1S) congenital myopathy
Acta Neuropathologica 2016cited by 135position: middledoi
Altered Splicing of the BIN1 Muscle-Specific Exon in Humans and Dogs with Highly Progressive Centronuclear Myopathy
PLoS Genetics 2013cited by 70position: firstdoi
Mutation spectrum in the large GTPase dynamin 2, and genotype-phenotype correlation in autosomal dominant centronuclear myopathy
Human Mutation 2012cited by 137position: firstdoi

Grants

No grants ingested yet.

Frequent collaborators

Jocelyn Laporte · Centre National de la Recherche Scientifique3 papers (2013–2024)Susan Treves · University of Ferrara2 papers (2018–2024) · 2 papers (2018–2024)Mohammad Ali Faghihi · United States Department of Commerce1 papers (2019–2019) · 1 papers (2013–2013)Ulrike Schara · KU Leuven1 papers (2013–2013)Hugues Jacobs · Centre National de la Recherche Scientifique1 papers (2018–2018) · 1 papers (2019–2019)Nasim Vasli · Centre for Addiction and Mental Health1 papers (2013–2013) · 1 papers (2018–2018)G. Diane Shelton · University of California San Diego1 papers (2013–2013) · 1 papers (2024–2024) · 1 papers (2019–2019) · 1 papers (2019–2019)Joachim Weis · Westfälische Hochschule1 papers (2013–2013) · 1 papers (2024–2024) · 1 papers (2019–2019) · 1 papers (2013–2013)Thomas Anderson · University of Otago1 papers (2013–2013)Céline Tard · Ludwig-Maximilians-Universität München1 papers (2024–2024)