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Barbara McDonough

Harvard University · US
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Area of research
Cardiology and Cardiovascular Medicine · Molecular Biology
Research interest
Research interests include Cardiomyopathy and Myosin Studies, Cardiovascular Effects of Exercise, Congenital heart defects research, and Cardiac electrophysiology and arrhythmias.
h-index
27
citations
8,437
works
67
NIH funding
primary concept
Medicine
email

Recent publications

Cardiac fibroblast BAG3 regulates TGFBR2 signaling and fibrosis in dilated cardiomyopathy
Journal of Clinical Investigation 2025cited by 13position: middledoi
Genetic therapies for cardiomyopathy: survey of attitudes of the patient community for the CureHeart project
European Journal of Human Genetics 2024cited by 10position: middledoi
Increased endothelial sclerostin caused by elevated DSCAM mediates multiple trisomy 21 phenotypes
Journal of Clinical Investigation 2024cited by 4position: middledoi
Genetic Contribution to End-Stage Cardiomyopathy Requiring Heart Transplantation
Circulation Genomic and Precision Medicine 2023cited by 11position: middledoi
Pathogenic variants damage cell composition and single cell transcription in cardiomyopathies
Science 2022cited by 233position: middledoi
Damaging variants in FOXI3 cause microtia and craniofacial microsomia
Genetics in Medicine 2022cited by 21position: middledoi
Discordant clinical features of identical hypertrophic cardiomyopathy twins
Proceedings of the National Academy of Sciences 2021cited by 32position: middledoi
Contribution of Noncanonical Splice Variants to <i>TTN</i> Truncating Variant Cardiomyopathy
Circulation Genomic and Precision Medicine 2021cited by 27position: middledoi
Cells of the adult human heart
Nature 2020cited by 1,739position: middledoi
Founder Mutation in N Terminus of Cardiac Troponin I Causes Malignant Hypertrophic Cardiomyopathy
Circulation Genomic and Precision Medicine 2020cited by 17position: middledoi
Hypertrophic cardiomyopathy mutations in <i>MYBPC3</i> dysregulate myosin
Science Translational Medicine 2019cited by 214position: middledoi
A gene-centric strategy for identifying disease-causing rare variants in dilated cardiomyopathy
Genetics in Medicine 2018cited by 31position: middledoi
Identification of pathogenic gene mutations in <i>LMNA</i> and <i>MYBPC3</i> that alter RNA splicing
Proceedings of the National Academy of Sciences 2017cited by 98position: middledoi
A Comparison of Whole Genome Sequencing to Multigene Panel Testing in Hypertrophic Cardiomyopathy Patients
Circulation Cardiovascular Genetics 2017cited by 92position: middledoi
<i>THSD1</i>(Thrombospondin Type 1 Domain Containing Protein 1) Mutation in the Pathogenesis of Intracranial Aneurysm and Subarachnoid Hemorrhage
Stroke 2016cited by 56position: middledoi
5′RNA-Seq identifies Fhl1 as a genetic modifier in cardiomyopathy
Journal of Clinical Investigation 2014cited by 68position: middledoi
Nationwide Study on Hypertrophic Cardiomyopathy in Iceland
Circulation 2014cited by 67position: middledoi
<i>UBQLN2</i> mutation causing heterogeneous X‐linked dominant neurodegeneration
Annals of Neurology 2014cited by 63position: middledoi
The Congenital Heart Disease Genetic Network Study
Circulation Research 2013cited by 167position: middledoi
<scp><i>HOXA</i></scp><i>2</i>Haploinsufficiency in Dominant Bilateral Microtia and Hearing Loss
Human Mutation 2013cited by 52position: middledoi
Truncations of Titin Causing Dilated Cardiomyopathy
New England Journal of Medicine 2012cited by 1,464position: middledoi
Functional effects of the TMEM43 Ser358Leu mutation in the pathogenesis of arrhythmogenic right ventricular cardiomyopathy
BMC Medical Genetics 2012cited by 21position: middledoi

Grants

No grants ingested yet.

Frequent collaborators

Christine E. Seidman · Harvard University15 papers (2012–2024)Steven R. DePalma · Harvard University11 papers (2013–2024)Jonathan G. Seidman · Harvard University10 papers (2013–2025)Joshua Gorham · MACOM (United States)7 papers (2014–2025)Yuri Kim · The University of Texas Southwestern Medical Center3 papers (2021–2025)Lien Lam · Netherlands Heart Institute3 papers (2017–2021)Hiroko Wakimoto · Harvard University3 papers (2014–2024)Neal K. Lakdawala · Harvard University3 papers (2017–2021)Calum A. MacRae · Harvard University3 papers (2016–2017)Diane Fatkin · St Vincent's Clinic3 papers (2017–2021)Jon A. L. Willcox · Harvard University3 papers (2021–2024)Daniel Quiat · The University of Texas Southwestern Medical Center3 papers (2021–2024)Daniel Reichart · Harvard University2 papers (2023–2024)Kaoru Ito · RIKEN Center for Integrative Medical Sciences2 papers (2017–2021) · 2 papers (2014–2017) · 2 papers (2021–2024)Christine E. Seidman · Brigham and Women's Hospital2 papers (2017–2025)Carolyn Y. Ho · Brigham and Women's Hospital2 papers (2017–2021)Kemar Brown · Massachusetts General Hospital2 papers (2024–2025)Gavin Y. Oudit · University of Alberta2 papers (2023–2025)
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