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James M. Polke

National Hospital for Neurology and Neurosurgery ·
Area of research
Cellular and Molecular Neuroscience · Neurology
Research interest
Research interests include Hereditary Neurological Disorders, Genetic Neurodegenerative Diseases, Mitochondrial Function and Pathology, and Neurological diseases and metabolism.
h-index
35
citations
4,988
works
114
NIH funding
primary concept
email

Recent publications

Adaptive Long‐Read Sequencing Reveals <scp>GGC</scp> Repeat Expansion in <scp><i>ZFHX3</i></scp> Associated with Spinocerebellar Ataxia Type 4
Movement Disorders 2024cited by 47position: middledoi
Whole genome sequencing increases the diagnostic rate in Charcot-Marie-Tooth disease
Brain 2024cited by 37position: middledoi
Role of the repeat expansion size in predicting age of onset and severity in RFC1 disease
Brain 2024cited by 28position: middledoi
Normal and pathogenic variation of <i>RFC1</i> repeat expansions: implications for clinical diagnosis
Brain 2023cited by 70position: middledoi
Genetic analysis and natural history of Charcot-Marie-Tooth disease CMTX1 due to <i>GJB1</i> variants
Brain 2023cited by 33position: middledoi
Mutations in alpha‐B‐crystallin cause autosomal dominant axonal Charcot–Marie–Tooth disease with congenital cataracts
European Journal of Neurology 2023cited by 11position: middledoi
Plasma GFAP in presymptomatic and symptomatic familial Alzheimer’s disease: a longitudinal cohort study
Journal of Neurology Neurosurgery & Psychiatry 2022cited by 46position: middledoi
Plasma amyloid-β ratios in autosomal dominant Alzheimer’s disease: the influence of genotype
Brain 2021cited by 34position: middledoi
Charcot-Marie-Tooth disease type 2CC due to<i>NEFH</i>variants causes a progressive, non-length-dependent, motor-predominant phenotype
Journal of Neurology Neurosurgery & Psychiatry 2021cited by 16position: middledoi
Cerebellar ataxia, neuropathy, vestibular areflexia syndrome due to RFC1 repeat expansion
Brain 2020cited by 220position: middledoi
Plasma phospho-tau181 in presymptomatic and symptomatic familial Alzheimer’s disease: a longitudinal cohort study
Molecular Psychiatry 2020cited by 122position: middledoi
Natural history of Charcot-Marie-Tooth disease type 2A: a large international multicentre study
Brain 2020cited by 89position: middledoi
Biallelic expansion of an intronic repeat in RFC1 is a common cause of late-onset ataxia
Nature Genetics 2019cited by 578position: middledoi
Autosomal dominant optic atrophy and cataract “plus” phenotype including axonal neuropathy
Neurology Genetics 2019cited by 15position: middledoi
Author Correction: Biallelic expansion of an intronic repeat in RFC1 is a common cause of late-onset ataxia
Nature Genetics 2019cited by 14position: middledoi
Genetic and clinical characteristics of<i>NEFL</i>-related Charcot-Marie-Tooth disease
Journal of Neurology Neurosurgery & Psychiatry 2017cited by 43position: middledoi

Grants

No grants ingested yet.

Frequent collaborators

Henry Houlden · University College London Hospitals NHS Foundation Trust5 papers (2017–2024)Andrea Cortese · University of Pavia4 papers (2019–2024)Mary M. Reilly · National Hospital for Neurology and Neurosurgery4 papers (2019–2024)Matilde Laurá · National Hospital for Neurology and Neurosurgery4 papers (2017–2024) · 4 papers (2017–2024)Julian Blake · Norfolk and Norwich University Hospital4 papers (2017–2024)Philip S.J. Weston · London School of Hygiene & Tropical Medicine3 papers (2020–2022)Nick C. Fox · Hospital Universitario Ramón y Cajal3 papers (2020–2022)Kaj Blennow · First Affiliated Hospital of Anhui Medical University3 papers (2020–2022)Stephan Züchner · University of Miami3 papers (2017–2024)Antoinette O’Connor · Trinity College Dublin3 papers (2020–2022)Teresa Poole · London School of Hygiene & Tropical Medicine3 papers (2020–2022)Emily K. Abel · UCLA Health3 papers (2020–2022)Amanda Heslegrave · UK Dementia Research Institute3 papers (2020–2022)Henrik Zetterberg · Indian Institute of Science Bangalore3 papers (2020–2022)Natalie S. Ryan · London School of Hygiene & Tropical Medicine3 papers (2020–2022)Alexander M. Rossor · Guy's and St Thomas' NHS Foundation Trust3 papers (2021–2024)Michael G. Hanna · Murdoch Children's Research Institute2 papers (2017–2019)Nicholas J. Ashton · Alzheimer's Association2 papers (2020–2022)Mariola Skorupinska · The Ohio State University Wexner Medical Center2 papers (2021–2024)