Area of research
Pulmonary and Respiratory Medicine · Physiology
Research interest
Research focused on Cystic fibrosis transmembrane conductance regulator and Cystic fibrosis, with related work in Chronic bronchitis, COPD, Ivacaftor. Notable publications include 'Acquired Cystic Fibrosis Transmembrane Conductance Regulator Dysfunction in the Lower Airways in COPD', 'Cigarette Smoke Induces Systemic Defects in Cystic Fibrosis Transmembrane Conductance Regulator Function', and 'A Pharmacologic Approach to Acquired Cystic Fibrosis Transmembrane Conductance Regulator Dysfunction in Smoking Related Lung Disease'.
Ribosomal frameshifting selectively modulates the assembly, function, and pharmacological rescue of a misfolded CFTR variant
Chronic Coinfection with Pseudomonas aeruginosa and Normal Colony Staphylococcus aureus Causes Lung Structural Damage in the Cystic Fibrosis Rat
Association between biomarkers of tobacco smoke exposure and clinical efficacy of ivacaftor in the G551D observational trial (GOAL)
Neonicotinoid pesticides impair mucociliary clearance, explaining respiratory harm
Nicotine aerosols diminish airway CFTR function and mucociliary clearance
Evaluation of a novel CFTR potentiator in COPD ferrets with acquired CFTR dysfunction
Airway remodeling in ferrets with cigarette smoke-induced COPD using µCT imaging
<i>Haemophilus influenzae</i>persists in biofilm communities in a smoke-exposed ferret model of COPD
Excess mucus viscosity and airway dehydration impact COPD airway clearance
Vaporized E-Cigarette Liquids Induce Ion Transport Dysfunction in Airway Epithelia
Heme scavenging reduces pulmonary endoplasmic reticulum stress, fibrosis, and emphysema
A Neutralizing Aptamer to TGFBR2 and miR-145 Antagonism Rescue Cigarette Smoke- and TGF-β-Mediated CFTR Expression
Acquired Cystic Fibrosis Transmembrane Conductance Regulator Dysfunction and Radiographic Bronchiectasis in Current and Former Smokers: A Cross-Sectional Study
Roflumilast reverses CFTR-mediated ion transport dysfunction in cigarette smoke-exposed mice
Not simply the lesser of two evils
The Cystic Fibrosis Transmembrane Conductance Regulator Potentiator Ivacaftor Augments Mucociliary Clearance Abrogating Cystic Fibrosis Transmembrane Conductance Regulator Inhibition by Cigarette Smoke
A ferret model of COPD-related chronic bronchitis
Pilot evaluation of ivacaftor for chronic bronchitis
Therapeutic Approaches to Acquired Cystic Fibrosis Transmembrane Conductance Regulator Dysfunction in Chronic Bronchitis.
Acquired Cystic Fibrosis Transmembrane Conductance Regulator Dysfunction in Chronic Bronchitis and Other Diseases of Mucus Clearance
Recovery of Acquired Cystic Fibrosis Transmembrane Conductance Regulator Dysfunction after Smoking Cessation
Impact of heterozygote CFTR Mutations in COPD patients with Chronic Bronchitis
Acquired Cystic Fibrosis Transmembrane Conductance Regulator Dysfunction in the Lower Airways in COPD
Cigarette Smoke Induces Systemic Defects in Cystic Fibrosis Transmembrane Conductance Regulator Function
Cigarette smoke and CFTR: implications in the pathogenesis of COPD
Cystic Fibrosis Transmembrane Conductance Regulator Activation by Roflumilast Contributes to Therapeutic Benefit in Chronic Bronchitis
A Pharmacologic Approach to Acquired Cystic Fibrosis Transmembrane Conductance Regulator Dysfunction in Smoking Related Lung Disease