← back to search

Nigel F. Clarke

The University of Adelaide · AU
Area of research
Molecular Biology · Cardiology and Cardiovascular Medicine
Research interest
Research interests include Muscle Physiology and Disorders, Cardiomyopathy and Myosin Studies, Neurogenetic and Muscular Disorders Research, and Genetic Neurodegenerative Diseases.
h-index
44
citations
6,876
works
146
NIH funding
primary concept
email

Recent publications

Congenital Titinopathy: Comprehensive characterization and pathogenic insights
Annals of Neurology 2018cited by 160position: middledoi
Dysfunctional sarcomere contractility contributes to muscle weakness in <i>ACTA1</i>‐related nemaline myopathy (NEM3)
Annals of Neurology 2018cited by 35position: middledoi
Improving genetic diagnosis in Mendelian disease with transcriptome sequencing
Science Translational Medicine 2017cited by 800position: middledoi
Cost-effectiveness of massively parallel sequencing for diagnosis of paediatric muscle diseases
npj Genomic Medicine 2017cited by 87position: middledoi
Variants in the Oxidoreductase PYROXD1 Cause Early-Onset Myopathy with Internalized Nuclei and Myofibrillar Disorganization
The American Journal of Human Genetics 2016cited by 106position: middledoi
Mutation‐specific effects on thin filament length in thin filament myopathy
Annals of Neurology 2016cited by 71position: middledoi
Diagnosis and etiology of congenital muscular dystrophy: We are halfway there
Annals of Neurology 2016cited by 70position: middledoi
Variants in <i>SLC18A3</i> , vesicular acetylcholine transporter, cause congenital myasthenic syndrome
Neurology 2016cited by 63position: middledoi
Targeted Re-Sequencing Emulsion PCR Panel for Myopathies: Results in 94 Cases
Journal of Neuromuscular Diseases 2016cited by 20position: middledoi
Use of Whole-Exome Sequencing for Diagnosis of Limb-Girdle Muscular Dystrophy
JAMA Neurology 2015cited by 201position: lastdoi
Mutations in<i>PIGY</i>: expanding the phenotype of inherited glycosylphosphatidylinositol deficiencies
Human Molecular Genetics 2015cited by 73position: lastdoi
Expanding the phenotype of GMPPB mutations
Brain 2015cited by 62position: middledoi
Muscle weakness in<i>TPM3</i>-myopathy is due to reduced Ca<sup>2+</sup>-sensitivity and impaired acto-myosin cross-bridge cycling in slow fibres
Human Molecular Genetics 2015cited by 56position: lastdoi
Leiomodin-3 dysfunction results in thin filament disorganization and nemaline myopathy
Journal of Clinical Investigation 2014cited by 203position: lastdoi
Mutation Update: The Spectra of Nebulin Variants and Associated Myopathies
Human Mutation 2014cited by 141position: middledoi
Mutation Update and Genotype-Phenotype Correlations of Novel and Previously Described Mutations in<i>TPM2</i>and<i>TPM3</i>Causing Congenital Myopathies
Human Mutation 2014cited by 110position: middledoi
Phenotypic and molecular insights into spinal muscular atrophy due to mutations in BICD2
Brain 2014cited by 98position: middledoi
Endogenous Glucuronyltransferase Activity of LARGE or LARGE2 Required for Functional Modification of α-Dystroglycan in Cells and Tissues
Journal of Biological Chemistry 2014cited by 22position: middledoi
Approach to the diagnosis of congenital myopathies
Neuromuscular Disorders 2013cited by 322position: middledoi
Mutations in KLHL40 Are a Frequent Cause of Severe Autosomal-Recessive Nemaline Myopathy
The American Journal of Human Genetics 2013cited by 223position: middledoi
Mutations in BICD2 Cause Dominant Congenital Spinal Muscular Atrophy and Hereditary Spastic Paraplegia
The American Journal of Human Genetics 2013cited by 190position: middledoi
Identification of KLHL41 Mutations Implicates BTB-Kelch-Mediated Ubiquitination as an Alternate Pathway to Myofibrillar Disruption in Nemaline Myopathy
The American Journal of Human Genetics 2013cited by 164position: middledoi
Genotype-phenotype correlations in recessive RYR1-related myopathies
Orphanet Journal of Rare Diseases 2013cited by 126position: middledoi
Neuromuscular junction abnormalities in DNM2-related centronuclear myopathy
Journal of Molecular Medicine 2013cited by 81position: middledoi
Recent advances in nemaline myopathy
Current Opinion in Neurology 2013cited by 80position: lastdoi
K7del is a common TPM2 gene mutation associated with nemaline myopathy and raised myofibre calcium sensitivity
Brain 2013cited by 54position: lastdoi
Troponin activator augments muscle force in nemaline myopathy patients with nebulin mutations
Journal of Medical Genetics 2013cited by 49position: middledoi
Young Australian adults with NF1 have poor access to health care, high complication rates, and limited disease knowledge
American Journal of Medical Genetics Part A 2013cited by 41position: middledoi
Consensus Statement on Standard of Care for Congenital Myopathies
Journal of Child Neurology 2012cited by 190position: middledoi
Mapping domains and mutations on the skeletal muscle ryanodine receptor channel
Trends in Molecular Medicine 2012cited by 50position: middledoi

Grants

No grants ingested yet.

Frequent collaborators

Kathryn N. North · Loughborough University12 papers (2013–2017)Nigel G. Laing · Pathwest Laboratory Medicine7 papers (2013–2017)Gina O’Grady · Starship Children's Health6 papers (2015–2017)Daniel G. MacArthur · Garvan Institute of Medical Research6 papers (2015–2017)Alan H. Beggs · Boston Children's Hospital6 papers (2013–2018)Coen A. C. Ottenheijm · University of Arizona5 papers (2013–2018)Sandra T. Cooper · The University of Sydney5 papers (2015–2017)Sarah A. Sandaradura · The University of Sydney5 papers (2013–2017)Monkol Lek · Yale University5 papers (2015–2016)Leigh B. Waddell · The University of Sydney5 papers (2015–2016)Emily C. Oates · UNSW Sydney4 papers (2013–2016)Michaela Yuen · The University of Sydney4 papers (2015–2018) · 4 papers (2013–2018)Roula Ghaoui · South Australia Pathology4 papers (2015–2016)Mark R. Davis · McGill University Health Centre4 papers (2015–2017)Carsten G. Bönnemann · National Institutes of Health4 papers (2013–2016)Josine M. de Winter · University of Arizona4 papers (2013–2018)J.H. Hwang · Children's Hospital at Westmead3 papers (2012–2013)Biljana Ilkovski · Children's Hospital at Westmead3 papers (2013–2015) · 3 papers (2013–2016)